Pastor Navarro Teresa, Verges Prosper Alexandre, Planelles Gómez Jorge, Pérez Ebri Maria Luisa, Llorente Domenech Rosa, Osca García Jose Manuel, Gil Salom Manuel
Urology Department, University Hospital Doctor Peset,Valencia, Spain.
Arch Esp Urol. 2013 Apr;66(3):305-7.
To report a case of paratesticular rhadomyosarcoma and to perform a bibliographic review.
We report the case of a 16-year-old male referred to our Department because of a left paratesticular hard tumor with progressive growth. Ultrasound examination showed a paratesticular heterogeneous mass with Internal flow on Doppler.
The patient underwent left inguinal orchiectomy, with pathological diagnosis of rhabdomyosarcoma. He refused adjuvant chemotherapy. After being disease-free for 13 months, he presented with left colic pain. Ultrasound and CT examinations showed a left paraaortic retroperitoneal mass causing grade III ureterohydronephrosis, and lung metastases. Despite rescue chemotherapy treatment, there was no response and the abdominal mass progressed. A surgical approach was not possible since patient showed a rapid clinical worsening leading to his death a few weeks later.
Paratesticular sarcomas are very uncommon tumors with poor prognosis.
报告1例睾丸旁横纹肌肉瘤病例并进行文献复习。
我们报告1例16岁男性因左侧睾丸旁硬性肿瘤进行性生长转诊至我科。超声检查显示睾丸旁不均匀肿块,多普勒检查有内部血流信号。
患者接受了左侧腹股沟睾丸切除术,病理诊断为横纹肌肉瘤。他拒绝辅助化疗。在无病生存13个月后,他出现左侧绞痛。超声和CT检查显示左腹主动脉旁腹膜后肿块导致Ⅲ级输尿管肾盂积水及肺转移。尽管进行了挽救性化疗,但无反应,腹部肿块进展。由于患者临床迅速恶化,几周后死亡,无法采取手术治疗。
睾丸旁肉瘤是非常罕见的肿瘤,预后较差。