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肺泡旁睾丸横纹肌肉瘤误诊为附睾炎:病例报告及文献复习

Alveolar paratesticular rhabdomyosarcoma mimicing epididymitis: Case report and literature review.

作者信息

Lei W-H, Wu Wen-Feng, Zhen Jin-Yang, Li Yang-Hui, Li Jie, Xin Jun

机构信息

Department of Medicine, Lishui Central Hospital, Lishui, Zhejiang Province Department of Urology Department of Pathology, The First Hospital of Fujian Medical University, Quanzhou, Fujian, China.

出版信息

Medicine (Baltimore). 2018 Jun;97(25):e11164. doi: 10.1097/MD.0000000000011164.

DOI:10.1097/MD.0000000000011164
PMID:29924027
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC6024466/
Abstract

RATIONALE

Most patients with paratesticular rhabdomyosarcoma may typically present as a unilateral, painless palpable scrotum mass. However, only a few cases of RMS presenting as painful edema of the scrotum mimicing epididymitis. We herein report an unusual case of alveolar paratesticular rhabdomyosarcoma misdiagnosed as epididymitis.

PATIENT CONCERNS

A 19-year-old adolescent, presented to urologist with painful swelling of the scrotum on the left side over the preceding several days. Antibiotics were administered by physician for two months and the pain improved, but the swelling did not fade.

DIAGNOSES

Alveolar praratesticular rhabdomyosarcoma.

INTERVENTIONS

A left, soft tissue mass in the scrotum without definite metastasis or lymphadenopathy was confirmed by computed tomography (CT) and magnetic resonance imaging. A radical left orchiectomy via the inguinal approach was performed successfully.

OUTCOME

The patient received 8 cycles of adjuvant chemotherapy, the patient remains recurrence- and metastasis-free at 13 months after surgery.

LESSONS

When paratesticular RMS is presenting with symptoms of epididymitis, this malignant tumor is usually overlooked. When patients complain of painful scrotal swelling, RMS arise from paratesticular tissue should be considered.

摘要

理论依据

大多数睾丸旁横纹肌肉瘤患者通常表现为单侧、无痛的可触及阴囊肿块。然而,仅有少数横纹肌肉瘤病例表现为类似附睾炎的阴囊疼痛性水肿。我们在此报告一例被误诊为附睾炎的罕见肺泡型睾丸旁横纹肌肉瘤病例。

患者情况

一名19岁青少年,在过去几天里因左侧阴囊疼痛肿胀就诊于泌尿科医生。医生给予抗生素治疗两个月,疼痛有所改善,但肿胀未消退。

诊断

肺泡型睾丸旁横纹肌肉瘤。

干预措施

通过计算机断层扫描(CT)和磁共振成像确认阴囊左侧有一个软组织肿块,无明确转移或淋巴结病变。成功实施了经腹股沟入路的左侧根治性睾丸切除术。

结果

患者接受了8个周期的辅助化疗,术后13个月仍无复发和转移。

经验教训

当睾丸旁横纹肌肉瘤表现为附睾炎症状时,这种恶性肿瘤通常会被忽视。当患者主诉阴囊疼痛肿胀时,应考虑睾丸旁组织发生的横纹肌肉瘤。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3674/6024466/86a5f67bfd05/medi-97-e11164-g005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3674/6024466/3e633a4765ba/medi-97-e11164-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3674/6024466/a0982ac37022/medi-97-e11164-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3674/6024466/eeeaa5d3bf9e/medi-97-e11164-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3674/6024466/b78b77b8749d/medi-97-e11164-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3674/6024466/86a5f67bfd05/medi-97-e11164-g005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3674/6024466/3e633a4765ba/medi-97-e11164-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3674/6024466/a0982ac37022/medi-97-e11164-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3674/6024466/eeeaa5d3bf9e/medi-97-e11164-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3674/6024466/b78b77b8749d/medi-97-e11164-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3674/6024466/86a5f67bfd05/medi-97-e11164-g005.jpg

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