Huge occipital myxomatous plexiform neurofibroma in the absence of neurofibromatosis.

A case of huge occipital myxomatous plexiform neurofibroma is presented. The lesion slowly enlarged since childhood and was associated with suboccipital bone hypoplasia. At operation the lesion was clearly originating from the occipital nerve and was totally excised. The case represents a rare occurrence of occipital myxomatous plexiform neurofibroma and suboccipital bone hypoplasia in the absence of evidence of neurofibromatosis.