Mortuza Shaikh, Esmaeli Bita, Bell Diana
Department of Pathology, Head and Neck Surgery, The University of Texas MD Anderson Cancer Center, Houston, Texas.
Head Neck. 2014 Apr;36(4):E36-8. doi: 10.1002/hed.23329. Epub 2013 Jun 1.
Schwannomas comprise 8% to 10% of all primary intracranial tumors. Primary intraorbital schwannomas are rare, accounting for 1% to 2% of all intracranial tumors. Schwannomas arise from Schwann cells in the myelin sheaths of sensory and cranial nerves.
We present the case of a 56-year-old white man blind since 1970 who presented to an outside hospital for a painful right eye. Physicians identified no clinical or radiologic features of neurofibromatosis.
The patient underwent enucleation; the final pathologic diagnosis was ancient schwannoma.
We describe herein a case of intrascleral schwannoma with ancient changes arising within the globe of the right eye occupying the subretinal space and completely replacing the vitreous body.
神经鞘瘤占所有原发性颅内肿瘤的8%至10%。原发性眶内神经鞘瘤罕见,占所有颅内肿瘤的1%至2%。神经鞘瘤起源于感觉神经和颅神经髓鞘中的施万细胞。
我们报告一例自1970年起失明的56岁白人男性病例,该患者因右眼疼痛就诊于外院。医生未发现神经纤维瘤病的临床或放射学特征。
患者接受了眼球摘除术;最终病理诊断为陈旧性神经鞘瘤。
我们在此描述一例右眼眼球内发生的伴有陈旧性改变的巩膜内神经鞘瘤,占据视网膜下间隙并完全取代玻璃体。