Zahir Shokouh Taghipour, Sharahjin Naser Sefidrokh, Dadgarnia Mohammad Hossein
Department of Pathology, Shahid Sadoughi University of Medical Sciences, Yazd, Islamic Republic of Iran.
BMJ Case Rep. 2013 Jun 3;2013:bcr2013009649. doi: 10.1136/bcr-2013-009649.
Synovial sarcoma is a rare form of malignant tumour and accounting approximately for 8% of all soft tissue sarcomas. Head and neck synovial sarcomas are uncommon and parapharyngeal space involvement is extremely rare. We report a case of synovial sarcoma in the parapharyngeal space of a 13-year-old boy with a history of neurofibromatosis presented with odynophagia, ptosis and left submandibular mass. The lesion extended from retrostyloid parapharyngeal space to the skull base and foramen jugular superiorly. The first clinical and radiological impressions were carotid jugular related tumours such as schwannoma and paraganglioma.
滑膜肉瘤是一种罕见的恶性肿瘤形式，约占所有软组织肉瘤的8%。头颈部滑膜肉瘤并不常见，累及咽旁间隙极为罕见。我们报告一例发生于一名13岁男孩咽旁间隙的滑膜肉瘤病例，该男孩有神经纤维瘤病病史，表现为吞咽痛、上睑下垂和左下颌下肿块。病变从茎突后咽旁间隙向上延伸至颅底和颈静脉孔。最初的临床和影像学印象是与颈动脉-颈静脉相关的肿瘤，如神经鞘瘤和副神经节瘤。
