Noh Dongsub, Park Chang-Kwon, Kwon Sun-Young
Department of Thoracic and Cardiovascular Surgery, School of Medicine, Keimyung University, Dae-gu, Republic of Korea.
Eur J Cardiothorac Surg. 2014 Mar;45(3):573-5. doi: 10.1093/ejcts/ezt304. Epub 2013 Jun 5.
It is well known that immunoglobulin G4 (IgG4)-related sclerosing disease usually occurs in the pancreas, bile duct and gall bladder, but not in the mediastinum, trachea or superior vena cava (SVC). In this case, a patient underwent mediastinal mass excision and trachea resection and repair for a mediastinal and intratracheal mass 15 years ago. This mass was diagnosed postoperatively as an inflammatory pseudotumour (plasma cell granuloma). Subsequently, a mass was found to have recurred in the SVC. We performed a mass excision and innominate vein to the right atrium auricle bypass operation. The mass was diagnosed as IgG4-related sclerosing disease. This patient is now disease and recurrence free.
众所周知，免疫球蛋白G4（IgG4）相关硬化性疾病通常发生于胰腺、胆管和胆囊，而非纵隔、气管或上腔静脉（SVC）。在此病例中，一名患者于15年前接受了纵隔肿物切除术及气管切除与修复术，以治疗纵隔及气管内肿物。该肿物术后被诊断为炎性假瘤（浆细胞肉芽肿）。随后，发现上腔静脉出现肿物复发。我们实施了肿物切除术及无名静脉至右心耳旁路手术。该肿物被诊断为IgG4相关硬化性疾病。该患者目前无疾病且未复发。
