Suppr超能文献

[与多伊奇-波特综合征相关的胸膜孤立性纤维瘤]

[Pleura solitary fibrous tumor associated with Doege-Potter Syndrome].

作者信息

Valenzuela Membrives M, Cassini Gómez de Cádiz L, Cueto Ladròn de Guevara A, García Pacheco M

机构信息

San Cecilio Klinikum, Sektion Pneumologie, Granada, Spanien.

出版信息

Pneumologie. 2013 Jun;67(6):340-3. doi: 10.1055/s-0033-1344079. Epub 2013 Jun 7.

Abstract

The Doege-Potter Syndrome is known as a combination of intrathoracic tumor associated to symptomatic hypoglycemia. Solitary Fibrous Tumor is a mesenchymal neoplasm. Initially, it was described in the pleura, however, it starts out in any organ or tissue at the expense of a stromal CD34+ cell. Most of the patients are asymptomatic at the time of diagnosis. Symptoms such as cough, dyspnea, chest pain, and hypoglycemia due to production of IGF-2 have been reported (Doegge- Potter Syndrome). Others described paraneoplastic profiles are hypertrophic osteoarthropathy and in some cases galactorrhea. We report on a case of a 77 year old patient with solitary fibrous tumor in the pleura as well as symptomatic hypoglycemia. The primary treatment is surgical resection, and a longtime monitoring is necessary because recurrences can occur even after a long period of remission.

摘要

多伊格-波特综合征是指胸腔内肿瘤合并症状性低血糖。孤立性纤维瘤是一种间叶性肿瘤。最初它被描述于胸膜,但它起源于任何器官或组织,由基质CD34+细胞发展而来。大多数患者在诊断时无症状。已报告的症状包括咳嗽、呼吸困难、胸痛以及因IGF-2产生导致的低血糖(多伊格-波特综合征)。其他描述的副肿瘤表现为肥大性骨关节病,在某些情况下还有溢乳。我们报告一例77岁患者,患有胸膜孤立性纤维瘤以及症状性低血糖。主要治疗方法是手术切除,并且需要长期监测,因为即使在长时间缓解后仍可能复发。

文献AI研究员

20分钟写一篇综述,助力文献阅读效率提升50倍。

立即体验

用中文搜PubMed

大模型驱动的PubMed中文搜索引擎

马上搜索

文档翻译

学术文献翻译模型,支持多种主流文档格式。

立即体验