Rizk Habib, Khazzaka Aline, Sebaaly Amer, Cherfan Maguy, Tomb Roland, Sarkis Riad
Department of Otolaryngology Head and Neck Surgery, Hotel Dieu de France Hospital, Beirut, Lebanon.
Case Rep Med. 2013;2013:512416. doi: 10.1155/2013/512416. Epub 2013 May 22.
We report the case of a 12-year-old girl, who consulted us with one-year history of an 8 mm nose lesion that was painless and firm upon palpation. The lesion was resected conservatively. Immunohistochemistry was in favor of a primitive neuroectodermal tumor (PNET)/Ewing's sarcoma lesion, excluding epithelial, lymphoid, and other tumors. After a second resection, our patient was referred to chemotherapy and has already undergone 9 cycles out of 14. The patient is to date with no evidence of persistent or recurrent disease. To our knowledge, this is the first description of a PNET arising in the nose.
我们报告了一名12岁女孩的病例,她因一个8毫米的鼻部病变前来就诊,该病变已有一年病史,触诊时无痛且质地坚硬。病变被保守切除。免疫组化结果支持原始神经外胚层肿瘤(PNET)/尤因肉瘤病变,排除上皮性、淋巴性及其他肿瘤。二次切除后,我们的患者接受了化疗,目前已完成14个周期中的9个周期。迄今为止,该患者没有持续性或复发性疾病的迹象。据我们所知,这是首次对发生于鼻部的PNET进行描述。