Badar Quratulain, Ali Nasir, Abbasi Nadeem, Ashraf Shamvil, Karsan Farrok, Hashmi Raheel
Department of Radiation Oncology, the Aga Khan University Hospital, Pakistan.
J Pak Med Assoc. 2010 Apr;60(4):314-5.
Ewing's sarcoma is the second most common primary tumour of bone in childhood. Less frequently it occurs in soft tissues. Ewing's sarcoma/primitive neuroectodermal tumour (ES/PNET) is an extra ordinarily rare primary tumour in the kidney. Only very few cases of primary renal Ewing's sarcoma have been reported in the literature to date. We present a case of primary right renal Ewing's sarcoma in a 13-year-old girl who was diagnosed as a case of stage IV ES/PNET of kidney with metastases to lung and liver. Right nephrectomy was done followed by adjuvant radiotherapy and chemotherapy with complete response to local and distant area.
尤因肉瘤是儿童期第二常见的原发性骨肿瘤。较少见的是它发生于软组织。尤因肉瘤/原始神经外胚层肿瘤（ES/PNET）是一种极其罕见的肾脏原发性肿瘤。迄今为止，文献中仅报道了极少数原发性肾尤因肉瘤病例。我们报告一例13岁女孩的原发性右肾尤因肉瘤，该病例被诊断为IV期肾ES/PNET，伴有肺和肝转移。行右肾切除术，随后进行辅助放疗和化疗，局部和远处均获得完全缓解。
