Akbulut Sami, Yilmaz Mehmet, Eris Cengiz, Kutlu Ramazan, Yilmaz Sezai
Liver Transplant Institute, Inonu University Faculty of Medicine, 44280 Malatya, Turkey.
Exp Clin Transplant. 2013 Jun;11(3):278-82. doi: 10.6002/ect.2012.0060.
Although rare, major congenital defects of the hepatic veins are detectable at autopsy, advanced, noninvasive imaging techniques such as Doppler ultrasonography and multislice computed tomography can accurately define these anomalies. One of these anomalies is congenital absence of the main right hepatic vein. We present a 21-year-old woman living-liver donor candidate with congenital absence of the right hepatic vein who underwent an extended right donor hepatectomy. She was tested for transplant compatibility with her 45-year-old brother, who had chronic liver failure secondary to hepatitis B. Multislice computed tomography revealed an absence of the right hepatic vein, and the right hepatic lobe was drained by 4 inferior hepatic veins with diameters ranging from 4 to 8.4 mm. An extended right-donor hepatectomy was performed. A common-large opening drainage reconstruction model that included all of the inferior hepatic veins and middle hepatic vein was created using the saphenous vein and an aortic homograft. There were no postoperative complications related to hepatic venous drainage thanks to the common-large opening model. We demonstrate that a right donor hepatectomy is feasible in congenital absence of the right hepatic vein solving the drainage problem using common-large opening reconstruction technique.
虽然罕见,但肝静脉的主要先天性缺陷在尸检时可被检测到,先进的非侵入性成像技术,如多普勒超声和多层计算机断层扫描,可以准确地确定这些异常情况。其中一种异常是右肝主静脉先天性缺如。我们报告一名21岁的女性活体肝供体候选者,其右肝静脉先天性缺如,接受了扩大右供肝切除术。她接受了与她45岁患有乙型肝炎继发慢性肝衰竭的哥哥的移植相容性检测。多层计算机断层扫描显示右肝静脉缺如,右肝叶由4条直径为4至8.4毫米的肝下静脉引流。进行了扩大右供肝切除术。使用大隐静脉和主动脉同种异体移植物创建了一个包括所有肝下静脉和肝中静脉的共同大开口引流重建模型。由于采用了共同大开口模型,术后没有出现与肝静脉引流相关的并发症。我们证明,在右肝静脉先天性缺如的情况下,采用共同大开口重建技术解决引流问题,右供肝切除术是可行的。