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先天性大理石样皮肤血管扩张症与青光眼。

Cutis marmorata telangiectatica congenita and glaucoma.

作者信息

Miranda I, Alonso M J, Jimenez M, Tomas-Barberan S, Ferro M, Ruiz R

机构信息

Department of Ophthalmology, Dr. Gutierrez Hospital 12 de Octubre, Madrid, Spain.

出版信息

Ophthalmic Paediatr Genet. 1990 Jun;11(2):129-32. doi: 10.3109/13816819009012958.

DOI:10.3109/13816819009012958
PMID:2377352
Abstract

A case of cutis marmorata telangiectatica congenita (CMTC) is described in association with congenital glaucoma. Approximately 68 cases of CMTC and only four cases associated with glaucoma have been reported. The type of glaucoma seems to be related to an abnormality of the filtration in the anterior angle, due to increased pressure in the episcleral vessels. The surgical treatment is trabeculectomy, and opening an alternative drainage pathway.

摘要

本文描述了一例先天性大理石样皮肤毛细血管扩张症(CMTC)合并先天性青光眼的病例。据报道,CMTC约有68例,而合并青光眼的仅有4例。青光眼的类型似乎与前房角滤过异常有关,这是由于巩膜上血管压力升高所致。手术治疗方法是小梁切除术,并开辟一条替代引流途径。

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