Nakada Yuki, Terui Ken, Kageyama Kazunori, Tsushima Yuko, Murakami Hiroshi, Soma Yasushi, Nigawara Takeshi, Sakihara Satoru
Department of Endocrinology and Metabolism, Hirosaki University Graduate School of Medicine, Japan.
Intern Med. 2013;52(12):1365-8. doi: 10.2169/internalmedicine.52.9543.
22q11.2 Deletion syndrome is recognized to be a major cause of congenital hypoparathyroidism, and affected patients exhibit a range of autoimmune characteristics. The syndrome becomes apparent in early childhood and is rarely diagnosed in adulthood. This report describes an adult case of 22q11.2 deletion syndrome first diagnosed in a 36-year-old woman with hypocalcemia caused by hypoparathyroidism and Hashimoto's thyroiditis. It is important to diagnose 22q11.2 deletion syndrome in adults because such patients are still at high risk for developing treatable diseases, such as hypocalcemia and autoimmune diseases.
22q11.2缺失综合征被认为是先天性甲状旁腺功能减退的主要原因,受影响的患者表现出一系列自身免疫特征。该综合征在儿童早期就会显现,在成年期很少被诊断出来。本报告描述了一例22q11.2缺失综合征的成年病例,该病例首次诊断于一名36岁女性,她患有甲状旁腺功能减退和桥本甲状腺炎引起的低钙血症。在成年人中诊断22q11.2缺失综合征很重要,因为这类患者仍有患可治疗疾病的高风险,如低钙血症和自身免疫性疾病。