Heart Institute (InCor) da Faculdade de Medicina da Universidade de São Paulo, São Paulo, Brazil.
Cardiovasc Pathol. 2013 Nov-Dec;22(6):503-4. doi: 10.1016/j.carpath.2013.05.001. Epub 2013 Jun 22.
A previously healthy 16-year-old woman experienced progressive dyspnea on exertion. The echocardiogram and cardiac magnetic resonance imaging showed a significant increase in cardiac chambers, severe biventricular systolic dysfunction, and prominent ventricular trabeculations suggesting noncompaction cardiomyopathy (NCC). The patient underwent heart transplantation 5 years after the NCC diagnosis, and the anatomopathological examination evidenced diffuse biventricular hypertrabeculation compromise, including the basal region of the biventricular wall. There is no consensus about the gold-standard diagnostic criteria, which demands a conceptual review and attention to another point: the relation of trabeculation volume and prognosis.
一位既往健康的 16 岁女性在活动时出现进行性呼吸困难。超声心动图和心脏磁共振成像显示心腔显著增大，双心室收缩功能严重障碍，室壁小梁明显突出，提示非致密性心肌病（NCC）。该患者在 NCC 诊断后 5 年接受了心脏移植，解剖病理学检查证实弥漫性双心室肥厚小梁受累，包括双心室壁的基底区域。目前尚无关于金标准诊断标准的共识，这需要进行概念性审查并关注另一个要点：小梁体积与预后的关系。
