Jatene Marcelo, Juaneda Ignacio, Miranda Rogerio Dos Anjos, Gato Rafaella, Marcial Miguel Lorenzo Barbero
Heart Institute, University of São Paulo, São Paulo, Brazil.
World J Pediatr Congenit Heart Surg. 2011 Oct 1;2(4):656-9. doi: 10.1177/2150135111414437.
A 9-year-old boy with congenital atresia of the left main coronary artery underwent myocardial revascularization. Coarctation of the aorta and ventricular septal defect were diagnosed at the age of 1 year. At age 7 years, the child presented with syncope while exercising. Preoperative evaluation included cardiac catheterization which revealed the unexpected finding of congenital atresia of the left main coronary artery with origin of the circumflex artery from the right coronary artery. Surgical correction included myocardial revascularization by means of left internal mammary artery graft to the anterior descending coronary artery, coarctation resection, and ventricular septal defect repair. The patient recovered uneventfully. We report the details of this extremely rare case with successful concomitant surgical management of the congenital coronary artery anomaly and the associated structural heart disease.
