Kerlin Bryce A, Haworth Kellie, Smoyer William E
Department of Pediatrics, The Ohio State University College of Medicine, Columbus, OH, USA,
Pediatr Nephrol. 2014 Jun;29(6):989-97. doi: 10.1007/s00467-013-2525-5. Epub 2013 Jun 28.
Childhood nephrotic syndrome (NS) is one of the most common pediatric kidney diseases, with an incidence of 2-7 per 100,000. Venous thromboembolism (VTE) is associated with significant morbidity and mortality, and occurs in ∼3 % of children with NS, though incidence approaches 25 % in high-risk groups. VTE etiology is multifactorial, with disease-associated coagulopathy thought to be a significant contributor. Other risks include age, disease severity, and treatment-related hazards, such as the presence of central venous catheters. Non-pharmacologic preventive measures such as ambulation and compression stockings are recommended for patients with identified VTE risks. Central venous catheters should be avoided whenever possible. Symptoms of VTE include venous catheter dysfunction, unilateral extremity symptoms, respiratory compromise, flank pain, and gross hematuria. When VTE is suspected, confirmatory imaging studies should be obtained, followed by appropriate laboratory evaluation and treatment. Therapeutic goals include limiting thrombus growth, extension, and embolization by early institution of anticoagulant therapy. Anticoagulation is recommended for a minimum of 3 months, but should be continued until NS remission is achieved. Further studies are necessary to identify VTE-risk biomarkers and optimal therapeutic regimens. Observational cohort studies are needed to identify VTE-risk groups who may benefit from thromboprophylaxis and to define disease-specific treatment algorithms.
儿童肾病综合征(NS)是最常见的儿科肾脏疾病之一,发病率为每10万人中有2至7例。静脉血栓栓塞症(VTE)与显著的发病率和死亡率相关,约3%的NS患儿会发生VTE,不过在高危组中发病率接近25%。VTE的病因是多因素的,与疾病相关的凝血病被认为是一个重要因素。其他风险包括年龄、疾病严重程度以及与治疗相关的危险因素,如中心静脉导管的存在。对于已确定有VTE风险的患者,建议采取非药物预防措施,如活动和穿加压袜。应尽可能避免使用中心静脉导管。VTE的症状包括静脉导管功能障碍、单侧肢体症状、呼吸功能不全、胁腹痛和肉眼血尿。怀疑有VTE时,应进行确诊性影像学检查,随后进行适当的实验室评估和治疗。治疗目标包括通过早期应用抗凝治疗来限制血栓生长、扩展和栓塞。建议抗凝至少3个月,但应持续至NS缓解。需要进一步研究以确定VTE风险生物标志物和最佳治疗方案。需要进行观察性队列研究,以确定可能从血栓预防中获益的VTE风险组,并确定针对特定疾病的治疗算法。