Firlinger I, Setinek U, Koller H, Feurstein P, Prosch H, Burghuber O C, Valipour A
Department of Respiratory and Critical Care Medicine, Ludwig-Boltzmann-Institute for COPD and Respiratory Epidemiology, Otto Wagner Hospital, Vienna, Austria.
Pneumologie. 2013 Jul;67(7):398-400. doi: 10.1055/s-0033-1344186. Epub 2013 Jul 4.
We report on a 55-year-old patient who was admitted to hospital because of recurrent pneumonia. CT imaging provided airway narrowing and mural thickening of the distal trachea and mainstem bronchi, compatible with endobronchial polypoid, toric-shaped changes of the distal tracheal wall spreading into both the left and right bronchial system. Bronchoscopy was performed and biopsies revealed the diagnosis of tracheobronchial amyloidosis. We performed a combination of bronchoscopic debulking and consecutive external beam radiation therapy with the result of no further progression of the disease, stable endobronchial situation, and functional improvements at a follow up at 6 months.
我们报告了一名55岁因复发性肺炎入院的患者。CT成像显示远端气管和主支气管气道狭窄及管壁增厚，符合支气管内息肉样改变，远端气管壁呈环形改变并蔓延至左右支气管系统。进行了支气管镜检查，活检确诊为气管支气管淀粉样变性。我们采用了支气管镜减瘤术联合连续外照射放疗，结果在6个月的随访中疾病无进一步进展，支气管内情况稳定，功能有所改善。
