Sanmillán Jose Luis, Plans Gerard, Vidal Noemí, Acebes Juan José
Neurosurgery Department, Bellvitge University Hospital , Hospitalet de Llobregat, Barcelona , Spain.
Br J Neurosurg. 2014 Jan;28(1):25-8. doi: 10.3109/02688697.2013.815320. Epub 2013 Jul 24.
Intracranial schwannomas not related to cranial nerves are uncommon brain tumours. Such tumours account for less than 1% of all surgically treated schwannomas. Only 79 cases have been reported in the literature.
We describe two cases treated in our centre. The patients are young women with seizures as a presenting symptom. Both underwent surgery with the presumptive diagnosis of benign brain tumour. Histopathological examination revealed the certain diagnosis of Schwannoma.
Good outcome was achieved with total excision of the tumour. Based on the literature, demographic data, clinical aspects, imaging features and theories on the possible origin of this rare tumour are discussed.
These tumours should be included in the differential diagnosis of supratentorial benign tumours in young adults. Total excision, whenever possible, is the treatment of choice.
与颅神经无关的颅内神经鞘瘤是罕见的脑肿瘤。此类肿瘤在所有接受手术治疗的神经鞘瘤中占比不到1%。文献中仅报道了79例。
我们描述了在我们中心治疗的两例病例。患者为年轻女性,以癫痫发作作为首发症状。两人均接受了手术,初步诊断为良性脑肿瘤。组织病理学检查确诊为神经鞘瘤。
肿瘤全切取得了良好的疗效。基于文献,讨论了人口统计学数据、临床特征、影像学特征以及关于这种罕见肿瘤可能起源的理论。
这些肿瘤应纳入年轻成人幕上良性肿瘤的鉴别诊断中。尽可能全切是首选治疗方法。