Rose Anna M, Kabiru Joy, Rose Geoffrey E
Department of Genetics, UCL Institute of Ophthalmology, London , EC1V 9EL , United Kingdom .
Orbit. 2013 Dec;32(6):384-6. doi: 10.3109/01676830.2013.815226. Epub 2013 Jul 29.
Haemangiopericytoma (HPC) is a rare soft tissue tumour of fibroblastic origin and is part of the solitary fibrous tumour spectrum. The tumour is generally considered to be benign, but can behave clinically as if sarcomatous -- with relentless infiltrative local growth. HPC generally presents in adulthood (median age 45 years for orbital disease) and is equally frequent in both sexes. HPC can arise in any site in the body and presents as a slowly growing, painless mass. We report a case of a 20 year old African male seen at Kikuyu Eye Unit, Kenya, with a 12 year history of a gradually enlarging, painless orbital mass. The patient underwent skin-sparing orbital exenteration with complete tumour excision; histology confirmed diagnosis of HPC.
血管外皮细胞瘤（HPC）是一种罕见的起源于成纤维细胞的软组织肿瘤，属于孤立性纤维性肿瘤谱系。该肿瘤通常被认为是良性的，但在临床上可能表现出肉瘤样行为——具有持续的浸润性局部生长。HPC一般在成年期出现（眼眶疾病的中位年龄为45岁），男女发病率相同。HPC可发生于身体的任何部位，表现为生长缓慢、无痛性肿块。我们报告一例20岁的非洲男性病例，该患者在肯尼亚基库尤眼科病房就诊，有一个逐渐增大、无痛性眼眶肿块的12年病史。患者接受了保留皮肤的眼眶内容剜除术并完整切除肿瘤；组织学检查确诊为HPC。
