Iruloh C, Keriakos R, Smith D J, Cleveland T
Jessop Wing and 2 Royal Hallamshire Hospital, Sheffi eld Teaching Hospitals, Sheffi eld, UK.
J Obstet Gynaecol. 2013 Aug;33(6):542-6. doi: 10.3109/01443615.2013.812622.
This is a literature review for management of angiomyolipoma (AML), lymphangioleiomyomatosis (LAM) and tuberous sclerosis (TS) during pregnancy, prompted by a case of a 23-year-old woman who presented with generalised itching at 31 weeks' gestation and was found to have a large vascular retroperitoneal mass in the lower pole of the left kidney. Magnetic resonance imaging (MRI) was suggestive of angiomyolipoma with multiple large aneurysms and haemorrhage within the tumour. She was delivered at 38 weeks by elective caesarean section, to avoid the risk of rupture and bleeding from the aneurysms during labour. Further imaging, with MR angiogram, computed tomography (CT) of the abdomen and pelvis and high resolution CT (HRCT) of the chest, confirmed lymphangioleiomyomatosis with left AML. She had embolisation of the AML performed twice, 8 weeks apart after delivery and subsequently had a left nephrectomy.
这是一篇关于妊娠期血管平滑肌脂肪瘤（AML）、淋巴管平滑肌瘤病（LAM）和结节性硬化症（TS）管理的文献综述，其起因是一名23岁女性的病例。该女性在妊娠31周时出现全身瘙痒，经检查发现左肾下极有一个巨大的血管性腹膜后肿块。磁共振成像（MRI）提示为血管平滑肌脂肪瘤，肿瘤内有多个大动脉瘤及出血。为避免分娩期间动脉瘤破裂和出血的风险，她在38周时接受了择期剖宫产。进一步的影像学检查，包括磁共振血管造影、腹部和盆腔计算机断层扫描（CT）以及胸部高分辨率CT（HRCT），确诊为淋巴管平滑肌瘤病合并左AML。她在产后8周间隔进行了两次AML栓塞治疗，随后接受了左肾切除术。
