Xie C, Shah N, Shah P L, Sandhu G
ENT Department, Charing Cross Hospital, Imperial College Trust, London, UK.
J Laryngol Otol. 2013 Sep;127(9):932-5. doi: 10.1017/S0022215113001746. Epub 2013 Aug 7.
Relapsing polychondritis is a multi-system autoimmune disease characterised by the inflammation and destruction of cartilaginous structures. The most common sites are the pinna, nose, laryngotracheobronchial tree and peripheral joints. Airway involvement occurs in up to half of patients affected, at any disease stage. It is the most severe and life-threatening aspect of the disease, and proves to be a therapeutic challenge.
This article reports our experience of performing laryngotracheal reconstruction in a patient with relapsing polychondritis. A review of the literature is presented, with a focused discussion of airway treatment options.
Laryngotracheal reconstruction for relapsing polychondritis was performed using hyoid bone pedicled on sternohyoid muscle.
Airway management in relapsing polychondritis can improve quality of life and palliate patients effectively.
复发性多软骨炎是一种多系统自身免疫性疾病，其特征为软骨结构的炎症和破坏。最常见的部位是耳廓、鼻子、喉气管支气管树和外周关节。在任何疾病阶段，多达一半的患者会出现气道受累。这是该疾病最严重且危及生命的方面，也是一个治疗挑战。
本文报告我们对一名复发性多软骨炎患者进行喉气管重建的经验。同时对文献进行综述，并重点讨论气道治疗方案。
采用以胸骨舌骨肌为蒂的舌骨对复发性多软骨炎患者进行喉气管重建。
复发性多软骨炎的气道管理可有效改善患者生活质量并缓解症状。
