Akan Okan, Cetin Selçuk, Eren Bülent, Durak Dilek, Türkmen Nursel, Gündoğmuş Umit Naci
Soud Lek. 2013 Jul;58(3):39-41.
Arrhythmogenic right ventricular dysplasia (ARVD) is both a myocardial disease that predominantly affects the right ventricle (RV) and one of the major causes of sudden death in the young and athletes. A 28-year-old man with no signicant medical history, applied to an emergency department with feeling very ill. After his initial examinations, electrocardiography (ECG) showed ventricular extra systoles and he was recommended for admission to a cardiology polyclinic. The next day, his condition worsened and he was dead on arrival at the hospital. A histological examination of heart samples, which were obtained from the RV and LV, revealed the massive replacement of myocardium by fibrous and mature adipose tissue in the RV. In this case, there were no symptoms, family and medical history and its clinical presentation was as an unexpected sudden death.
Arrhythmogenic right ventricular dysplasia, sudden cardiac death, autopsy.
致心律失常性右室发育不良（ARVD）是一种主要累及右心室（RV）的心肌病，也是年轻人和运动员猝死的主要原因之一。一名28岁无重大病史的男子因感觉身体不适前往急诊科就诊。初步检查后，心电图（ECG）显示室性早搏，他被建议入住心脏病专科门诊。第二天，他的病情恶化，到达医院时已死亡。对取自右心室和左心室的心脏样本进行组织学检查，发现右心室心肌被纤维组织和成熟脂肪组织大量替代。在这种情况下，没有症状、家族史和病史，其临床表现为意外猝死。
致心律失常性右室发育不良，心源性猝死，尸检
