Berishvili I I, Ragimov F R, Lebedeva T M, Vakhromeeva M N
Arkh Patol. 1990;52(5):21-7.
New anatomical criteria of the above malformation are created on the basis of the study of 63 hearts with the origin of aorta and lung artery from the right ventricle: the presence of the bulboventricular fold separating the mitral and semilunar valves; complete or partial delay of the subaortal cone movement to the left ventricle; the presence of the completely or partially formed proximal cone; underdevelopment of the left ventricle due to the complete or partial absence of its cone region; the only issue from the left ventricle is the proximal cone apertures or a part of the primary bulboventricular orifice; when the primary bulboventricular orifice is obturated the left ventricle is either deprived of the opening or has it in the form of noncommitted defect in the sinusal part of the interventricular septum; the anterior margins of the bulboventricular fold and cone septum are open and supraventricular comb is not formed; the interventricular septum defect formed due to failure of fusion between bulboventricular fold and cone septum connects the aorta with the right ventricle; aorta and lung artery start completely or partially from the right ventricle.
基于对63例主动脉和肺动脉起源于右心室的心脏的研究,建立了上述畸形的新解剖学标准:存在将二尖瓣和半月瓣分开的球室襞;主动脉下圆锥向左心室移动完全或部分延迟;存在完全或部分形成的近端圆锥;由于左心室圆锥区域完全或部分缺失,左心室发育不全;左心室的唯一出口是近端圆锥孔或部分原始球室孔;当原始球室孔闭塞时,左心室要么没有开口,要么在室间隔窦部有非限制性缺损形式的开口;球室襞和圆锥间隔的前缘开放,未形成室上嵴;由于球室襞和圆锥间隔融合失败形成的室间隔缺损将主动脉与右心室相连;主动脉和肺动脉完全或部分起源于右心室。