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儿童癫痫性脑病的诊断与管理

Diagnosis and management of epileptic encephalopathies in children.

作者信息

Jain Puneet, Sharma Suvasini, Tripathi Manjari

机构信息

Division of Pediatric Neurology, Department of Pediatrics, All India Institute of Medical Sciences, New Delhi 110029, India.

出版信息

Epilepsy Res Treat. 2013;2013:501981. doi: 10.1155/2013/501981. Epub 2013 Jul 22.

DOI:10.1155/2013/501981
PMID:23970964
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC3736403/
Abstract

Epileptic encephalopathies refer to a group of disorders in which the unremitting epileptic activity contributes to severe cognitive and behavioral impairments above and beyond what might be expected from the underlying pathology alone, and these can worsen over time leading to progressive cerebral dysfunction. Several syndromes have been described based on their electroclinical features (age of onset, seizure type, and EEG pattern). This review briefly describes the clinical evaluation and management of commonly encountered epileptic encephalopathies in children.

摘要

癫痫性脑病是指一组疾病，其中持续的癫痫活动导致严重的认知和行为障碍，超出了仅由潜在病理所预期的程度，并且这些障碍会随着时间的推移而恶化，导致进行性脑功能障碍。根据其电临床特征（发病年龄、癫痫发作类型和脑电图模式）已描述了几种综合征。本综述简要描述了儿童常见癫痫性脑病的临床评估和管理。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/47bb/3736403/fe132dcd3b9c/ERT2013-501981.004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/47bb/3736403/bdaa014a4fa3/ERT2013-501981.001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/47bb/3736403/fc110a761326/ERT2013-501981.002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/47bb/3736403/ae156e3b7acb/ERT2013-501981.003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/47bb/3736403/fe132dcd3b9c/ERT2013-501981.004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/47bb/3736403/bdaa014a4fa3/ERT2013-501981.001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/47bb/3736403/fc110a761326/ERT2013-501981.002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/47bb/3736403/ae156e3b7acb/ERT2013-501981.003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/47bb/3736403/fe132dcd3b9c/ERT2013-501981.004.jpg

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