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先天性左心梗阻性病变的干预与管理

Intervention and management of congenital left heart obstructive lesions.

作者信息

Schimke Amy, Majithia Arjun, Baumgartner Robert, French Amy, Goldberg David, Kuvin Jeffrey

机构信息

The CardioVascular Center, Division of Cardiology, Tufts Medical Center, 800 Washington Street, Box 315, Boston, MA, 02111, USA.

出版信息

Curr Treat Options Cardiovasc Med. 2013 Oct;15(5):632-45. doi: 10.1007/s11936-013-0260-7.

Abstract

While congenital heart defects are typically diagnosed in early childhood, depending on the severity of the lesion, they may not be recognized until later childhood or in adulthood. Left heart pressure loading lesions, including mitral valve stenosis, subaortic stenosis, valvular aortic stenosis, supravalvular aortic stenosis, and coarctation of the aorta, may be found as an isolated lesion or as a constellation together known as Shone syndrome. This review will highlight the literature published regarding the diagnosis, intervention, and long-term management of left heart pressure loading lesions.

摘要

虽然先天性心脏缺陷通常在儿童早期被诊断出来,但根据病变的严重程度,它们可能直到儿童后期或成年期才被发现。左心压力负荷性病变,包括二尖瓣狭窄、主动脉瓣下狭窄、瓣膜性主动脉瓣狭窄、瓣上主动脉瓣狭窄和主动脉缩窄,可能作为孤立病变被发现,也可能作为一组病变共同存在,即所谓的肖恩综合征。本综述将重点介绍已发表的关于左心压力负荷性病变的诊断、干预和长期管理的文献。

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