Adamczuk Dominika, Krzemień Grażyna, Szmigielska Agnieszka, Pierzchlewicz Anna, Roszkowska-Blaim Maria, Biejat Agnieszka, Dębska Małgorzata, Jabłońska-Jesionowska Monika
Katedra i Klinika Pediatrii i Nefrologii, WUM, Warszawa.
Med Wieku Rozwoj. 2013 Apr-Jun;17(2):174-8.
The most common causes of laryngeal stridor are laryngomalacia (60%), vocal cord paralysis (VCP) (10 %) and subglottic laryngeal stenosis. Majority of cases of VCP are idiopathic, less frequently it is the effect of abnormalities in central nervous system (Arnold - Chiari syndrome, hydrocephalus, neonatal hypoxia). Differential diagnosis should also include anomalies of aortic arch and its branches (vascular rings). The authors present two cases of neonatal congenital laryngeal stridor. In the first case the girl presented with VCP of unknown etiology. The perinatal period was normal, ultrasound of central nervous system and neurologic examination revealed no abnormalities. Due to sustained VCP in control laryngeal ultrasound examinations, tracheostomy was performed in the third month of life. In the second case, stridor was caused by laryngomalacia and subglottic laryngeal stenosis of first grade according to Meyer-Cotton scale (larynx lumen diameter <4 mm). The diagnosis was established by laryngotracheobronchoscopy. In both children angiotomography was performed and vascular ring was diagnosed (aberrant right subclavian artery). Vascular anomaly was suspected in barium X-ray. In both cases echocardiographic examination did not visualize the fourth vessel of the aortic arch. Chest X- rays were normal. Both children had no symptoms caused by vascular ring.
Diagnosis of congenital laryngeal stridor is an indication for complete evaluation to establish the cause of the airway obstruction. The differential diagnosis should include laryngomalacia, vocal cord paralysis, subglottic laryngeal stenosis, congenital anomalies of large vessels and abnormalities of the central nervous system.
喉喘鸣最常见的病因是喉软化症(60%)、声带麻痹(VCP)(10%)和声门下喉狭窄。大多数VCP病例是特发性的,较少见的是中枢神经系统异常(阿诺德-奇亚里综合征、脑积水、新生儿缺氧)的影响。鉴别诊断还应包括主动脉弓及其分支的异常(血管环)。作者介绍了两例新生儿先天性喉喘鸣病例。第一例中,女孩出现病因不明的VCP。围生期正常,中枢神经系统超声检查和神经学检查未发现异常。由于在对照喉超声检查中VCP持续存在,患儿在出生后第三个月进行了气管切开术。第二例中,喘鸣是由喉软化症和声门下喉狭窄引起的,根据迈耶-科顿量表为一级(喉腔直径<4mm)。通过喉镜气管支气管镜检查确诊。两名患儿均进行了血管造影并诊断出血管环(迷走右锁骨下动脉)。在钡剂X线检查中怀疑有血管异常。两例患儿的超声心动图检查均未显示主动脉弓的第四支血管。胸部X线检查正常。两名患儿均无血管环引起的症状。
先天性喉喘鸣的诊断需要进行全面评估以确定气道阻塞的原因。鉴别诊断应包括喉软化症、声带麻痹、声门下喉狭窄、大血管先天性异常和中枢神经系统异常。