Department of Cardiothoracic Surgery, Section of Pediatric Cardiothoracic Surgery, Yale School of Medicine, New Haven, Connecticut 06510, USA.
Ann Thorac Surg. 2013 Sep;96(3):1078-80. doi: 10.1016/j.athoracsur.2012.12.043.
We are reporting a rare case of papillary fibroelastoma of the tricuspid valve in an 8-year-old child who presented with pulmonary embolism. Echocardiography was instrumental in determining the source of the pulmonary embolism, but not in delineating between tumor and thrombus. Successful surgical resection of the mass was accomplished and good outcome was attained despite the delay in diagnosis and failure of medical management. A high index of suspicion for tumor involving the tricuspid valve is emphasized despite its rarity in children.
我们报告了一例罕见的 8 岁儿童三尖瓣乳头状纤维弹性瘤病例,该患儿表现为肺栓塞。超声心动图有助于确定肺栓塞的来源,但无法区分肿瘤和血栓。尽管诊断延迟且药物治疗失败,仍成功地进行了肿块的外科切除,获得了良好的结果。强调即使在儿童中罕见,也要高度怀疑累及三尖瓣的肿瘤。