Rizwan M M, Chhabra G, Mishra A, Kapadia S, Rai R, Gill H
Mian Muhammad Rizwan, Department of Internal Medicine, Prince George's Hospital, 3001 Hospital Drive, Cheverly, MD 20785; USA. Email:
Gulf J Oncolog. 2013 Jul;1(14):87-9.
Rosai-Dorfman Syndrome (RDD) is a rare, benign, self-limiting disorder which is characterized by the non-malignant proliferation of distinctive histiocytic cell within lymphatic system. RDD has been described as a dynamic entity in the spectrum of histiocytosis with non-Langerhans cell histiocytosis at one end and Langerhans cell histiocytosis at the other. The exact etiology of this disease is uncertain despite widespread search for infectious or immunological reasons. We present a case of purely cutaneous Rosai-Dorfman Syndrome presenting as abdominal wall swelling.
Rosai-Dorfman Disease, Lymphoma.
罗萨伊-多夫曼综合征（RDD）是一种罕见的、良性的、自限性疾病，其特征是淋巴系统内独特组织细胞的非恶性增殖。RDD被描述为组织细胞增生症谱中的一种动态实体，一端为非朗格汉斯细胞组织细胞增生症，另一端为朗格汉斯细胞组织细胞增生症。尽管广泛寻找感染或免疫方面的原因，但该疾病的确切病因仍不确定。我们报告一例以腹壁肿胀为表现的单纯皮肤型罗萨伊-多夫曼综合征病例。
罗萨伊-多夫曼病；淋巴瘤
