Pombo Castro María, Luaces Rey Ramón, Arenaz Búa Jorge, Santana-Mora Urbano, López-Cedrún Cembranos José Luís
*Resident, Department of Oral and Maxillofacial Surgery, A Coruña University Hospital, A Coruña, Spain. †Staff, Department of Oral and Maxillofacial Surgery, A Coruña University Hospital, A Coruña, Spain. ‡Staff, Department of Oral and Maxillofacial Surgery, Povisa Hospital, Vigo, Spain. §Chief, Department of Oral and Maxillofacial Surgery, A Coruña University Hospital, A Coruña, Spain. ‖Clinical Tutor, Department of Prosthodontics and Occlusion, University of Santiago de Compostela, A Coruña, Spain.
Implant Dent. 2013 Oct;22(5):460-4. doi: 10.1097/ID.0b013e3182a2b8d2.
Oral manifestations in ectodermal dysplasia include oligodontia, alveolar ridges hypoplasia, and others. Due to the special conditions in terms of unhealthy teeth and lack of bone, implant-supported rehabilitation seems to offer the most satisfactory outcome. A 27-year-old male diagnosed with ectodermal dysplasia was referred to our department for oral rehabilitation. Oral manifestations included oligodontia, maxillary and mandibular atrophy, mandibular alveolar ridge with knife-edge morphology, and conical teeth. Treatment planning consisted of a Le Fort I osteotomy with interpositional grafts, bilateral sinus lift, and placement of maxillary and mandibular inlay and onlay corticocancellous grafts, using autologous iliac crest bone. In the second surgery, all remaining teeth were removed and 11 endosteal implants were placed. Six months after implant placement, a bimaxillary fixed implant-supported prosthesis was delivered, maintaining a satisfactory esthetic and functional result after a 2-year follow-up. The use of combined preprosthetic techniques allows the placement of endosteal implants and a fixed implant-supported prosthesis in patients with oligodontia and ectodermal dysplasia, providing an esthetic and functional oral rehabilitation.
外胚层发育不全的口腔表现包括牙齿缺失、牙槽嵴发育不全等。由于牙齿不健康和骨量不足的特殊情况，种植体支持的修复似乎能提供最令人满意的效果。一名27岁被诊断为外胚层发育不全的男性被转诊至我科进行口腔修复。口腔表现包括牙齿缺失、上颌和下颌萎缩、呈刀刃状形态的下颌牙槽嵴以及锥形牙。治疗方案包括采用带植入物的勒福I型截骨术、双侧鼻窦提升术，以及使用自体髂骨进行上颌和下颌嵌体及覆盖植骨术。在第二次手术中，拔除了所有剩余牙齿并植入了11枚骨内种植体。种植体植入6个月后，交付了一副双颌固定种植体支持的假体，经过2年随访，保持了令人满意的美观和功能效果。联合使用修复前技术能够在牙齿缺失和外胚层发育不全的患者中植入骨内种植体并制作固定种植体支持的假体，从而实现美观和功能俱佳的口腔修复。
