Johns Dexton A
Department of Endodontics, Government Dental College, Calicut, Kerala, India.
J Indian Soc Pedod Prev Dent. 2013 Jul-Sep;31(3):184-7. doi: 10.4103/0970-4388.117978.
Freeman-Sheldon syndrome is a rare progressive myopathic disorder affecting the face, chest, and limbs. It is characterized by three basic abnormalities: microstomia with pouting lips, camptodactyly with ulnar deviation of the fingers, and talipes equinovarus. Presence of microstomia is always associated with practical difficulties of oral hygiene maintenance and increased susceptibility to caries. Patient as well as parental counseling is important in these cases. This case report presents a 7-year-old child with Freeman-Sheldon syndrome. Emphasis is given for the dental management of such children.
弗里曼-谢尔顿综合征是一种罕见的进行性肌病性疾病，影响面部、胸部和四肢。它具有三个基本异常特征：小口症伴撅嘴、手指屈曲挛缩伴尺侧偏斜以及马蹄内翻足。小口症的存在总是与口腔卫生维护的实际困难以及龋齿易感性增加相关。在这些病例中，对患者及其家长进行咨询很重要。本病例报告介绍了一名患有弗里曼-谢尔顿综合征的7岁儿童。重点是此类儿童的牙科治疗。
