Sandrock D, Merino M J, Scheffknecht B H, Neumann R D
Department of Nuclear Medicine, Warren G. Magnuson Clinical Center, National Institutes of Health, Bethesda, MD 20892.
Eur J Nucl Med. 1990;16(1):55-60. doi: 10.1007/BF01566013.
Two cases of Erdheim-Chester disease are presented: a 26-year-old white male patient with lipoidgranulomatosis of numerous long and flat bones and infiltration of pericardium, pleura, liver, spleen, thyroid, skin, conjunctiva, gingiva, and false vocal cord; and a 54-year-old white male with involvement of bones, orbits, brain, pericardium, and retroperitoneum. The scintigraphic findings in this disease are described, and a comprehensive review of the 27 previously reported cases is given including an assessment of the value of scintigraphy for diagnosis and follow up of this rare disease.
本文报告了两例 Erdheim-Chester 病病例：一例为 26 岁白人男性患者，患有多处长骨和扁骨的类脂质肉芽肿，同时心包、胸膜、肝脏、脾脏、甲状腺、皮肤、结膜、牙龈及假声带均有浸润；另一例为 54 岁白人男性，病变累及骨骼、眼眶、脑、心包及腹膜后。文中描述了该病的闪烁扫描检查结果，并对先前报道的 27 例病例进行了全面回顾，包括评估闪烁扫描对这种罕见疾病诊断及随访的价值。
