功能性肾上腺皮质癌侵犯至右心房并导致库欣综合征

Kumar Santosh, Choudhary Gautam R, Pushkarna Arawat

Department of Urology, Postgraduate Institute of Medical Education and Research, Chandigarh, India.

J Clin Imaging Sci. 2013 Aug 31;3:32. doi: 10.4103/2156-7514.116186. eCollection 2013.

Adrenocortical carcinoma (ACC) is a rare malignancy with poor prognosis. Surgery is the only curative therapy available and overall 5-year survival for patients who undergo a complete resection is 32% to 48%. They are known to produce intravascular invasion and into the inferior vena cava (IVC) and in rare cases they may reach the right atrium. We report a case of functioning ACC extending into the inferior vena cava and right atrium in a female with Cushing's syndrome.

肾上腺皮质癌（ACC）是一种预后较差的罕见恶性肿瘤。手术是唯一可用的治愈性疗法，接受完整切除的患者总体5年生存率为32%至48%。已知它们会发生血管内侵犯并侵入下腔静脉（IVC），在罕见情况下，它们可能会延伸至右心房。我们报告一例患有库欣综合征的女性患者，其功能性肾上腺皮质癌延伸至下腔静脉和右心房。