Kahilogullari Gokmen, Tuna Hakan, Kuzu Isinsu, Unlu Agahan
Ankara University, Faculty of Medicine, Department of Neurosurgery, Ankara, Turkey.
Turk Neurosurg. 2013;23(4):575-7. doi: 10.5137/1019-5149.JTN.6026-12.0.
Eosinophilic granuloma is a rare disease belonging to the Langerhans' cell histiocytosis group. It accounts for only 1% of all tumor-like lesions of bone. A 6-year-old girl presented with proptosis, and a mass and pain in her right eye. Cranial computerized tomography and magnetic resonance imaging revealed a mass in her right orbital area. The patient was operated through a right frontotemporal craniotomy and orbitozygomatic osteotomy. The tumour was totally removed. The postoperative course was uneventful. Histopathological examination revealed a diagnosis of eosinophilic granuloma with typical Langerhans cells and eosinophylic leucocyte infiltration. We report an orbital eosinophilic granuloma case, which is rarely seen, and discuss its clinical and pathological features.
嗜酸性肉芽肿是一种罕见疾病，属于朗格汉斯细胞组织细胞增多症范畴。它仅占所有骨肿瘤样病变的1%。一名6岁女孩出现眼球突出，右眼有肿物及疼痛。头颅计算机断层扫描和磁共振成像显示其右眼眶区域有一个肿物。患者通过右额颞开颅术和眶颧截骨术接受手术。肿瘤被完全切除。术后过程顺利。组织病理学检查显示诊断为嗜酸性肉芽肿，伴有典型的朗格汉斯细胞和嗜酸性白细胞浸润。我们报告一例罕见的眼眶嗜酸性肉芽肿病例，并讨论其临床和病理特征。
