Al-Saleem Afnan, Al-Jobair Asma
Pediatric Dentistry Board Resident, Dental Department, Riyadh Military Hospital, Saudi Arabia.
Saudi Dent J. 2010 Oct;22(4):195-9. doi: 10.1016/j.sdentj.2010.07.001. Epub 2010 Jul 14.
Achondroplasia is the most common form of skeletal dysplasia dwarfism that manifests with stunted stature and disproportionate limb shortening. Achondroplasia is of dental interest because of its characteristic craniofacial features which include relative macrocephaly, depressed nasal bridge and maxillary hypoplasia. Presence of large head, implanted shunt, airway obstruction and difficulty in head control require special precautions during dental management. Craniofacial manifestations and considerations in dental management are presented in 11-year-old female patient with achondroplasia.
软骨发育不全是骨骼发育异常侏儒症最常见的形式，表现为身材矮小和四肢不成比例缩短。软骨发育不全在牙科领域备受关注，因为其具有特征性的颅面特征，包括相对巨头畸形、鼻梁凹陷和上颌发育不全。存在大头、植入分流器、气道阻塞和头部控制困难等情况，在牙科治疗期间需要特别预防措施。本文介绍了一名患有软骨发育不全的11岁女性患者的颅面表现及牙科治疗注意事项。
