Vagholkar Ketan, Dastoor Khojasteh
Department of Surgery, Dr. D. Y. Patil Medical College, Navi Mumbai, Maharashtra 400706, India ; Annapurna Niwas, 229 Ghantali Road, Thane 400602, India.
Case Rep Pediatr. 2013;2013:532910. doi: 10.1155/2013/532910. Epub 2013 Sep 18.
Introduction. Congenital lumbar hernia is one of the rare types of hernias. Anomalies of the ribs, spine, and muscles which constitute the lumbocostovertebral syndrome in association with congenital lumbar hernia make it the rarest of entities. In addition, a multitude of other organ systems may be involved. Case Report. A case of congenital lumbar hernia associated with lumbocostovertebral syndrome is presented in view of its rarity and diagnostic and therapeutic challenges. Discussion. Anatomical background of congenital lumbar hernia associated with various other anomalies especially of the musculoskeletal structures is discussed. All cases of congenital lumbar hernia should be investigated for other congenital anomalies. Both open and laparoscopic approaches have been described for surgical treatment. Conclusion. Open surgical intervention is the mainstay of treatment taking into consideration the technical challenges posed by distorted anatomy due to the associated congenital anomalies.
引言。先天性腰疝是罕见的疝类型之一。构成腰肋椎综合征的肋骨、脊柱和肌肉异常与先天性腰疝相关，使其成为最罕见的病症。此外，许多其他器官系统可能受累。病例报告。鉴于先天性腰疝合并腰肋椎综合征的罕见性以及诊断和治疗挑战，现报告一例。讨论。讨论了与各种其他异常尤其是肌肉骨骼结构异常相关的先天性腰疝的解剖学背景。所有先天性腰疝病例均应检查是否存在其他先天性异常。手术治疗已描述了开放和腹腔镜两种方法。结论。考虑到相关先天性异常导致解剖结构扭曲带来的技术挑战，开放手术干预是主要的治疗方法。
