Baudet E, Hafez A, Choussat A, Dias da Silva E, Laborde N, Collot M, Panès F, Roques X
Thorac Cardiovasc Surg. 1985 Dec;33(6):366-70. doi: 10.1055/s-2007-1014170.
A case of isolated anomalous origin of the right pulmonary artery from the ascending aorta with severe pulmonary hypertension is reported. Surgical repair was achieved by anastomosis of the anomalous vessel to the pulmonary artery trunk using a continuous absorbable suture. Special emphasis is laid on the favorable postoperative evolution of the pulmonary hypertensive disease following the successful repair. The poor natural history of this uncommon congenital defect if untreated makes early corrective surgery imperative.
报告一例右肺动脉自升主动脉孤立性异常起源并伴有严重肺动脉高压的病例。通过使用连续可吸收缝线将异常血管与肺动脉主干吻合实现了手术修复。特别强调了成功修复后肺动脉高压疾病良好的术后进展情况。这种罕见的先天性缺陷若不治疗，其自然病程较差，因此早期进行矫正手术势在必行。
