Montroni Isacco, Sabattini Elena, Ramadori Eleonora, Koprivica Vidak, Ugolini Giampaolo, Locatelli Francesca, Ghignone Federico, Rosati Giancarlo, Taffurelli Mario, Pileri Stefano
University of Bologna, Bologna, Italy
University of Bologna, Bologna, Italy.
Int J Surg Pathol. 2014 Aug;22(5):434-7. doi: 10.1177/1066896913507599. Epub 2013 Oct 31.
Multicentric Castleman's disease is a rare condition of systemic nonclonal lymph node hyperplasia. Because of its strong association with human herpes virus 8 (HHV8), the multicentric, more aggressive, form may progress to Kaposi sarcoma or non-Hodgkin lymphoma. While surgery is curative in the treatment of localized Castleman's disease, operative treatment of the diffuse form has as yet been unsatisfactory. We report the case of a patient presenting with postprandial vomiting of 1 month duration consistent with partial small bowel obstruction secondary to terminal ileum intussusception. Resection of the small bowel showed a stenosing tumor triggering the intussusception. On pathological examination, the tumor was found to be composed of HHV8-positive plasmablastic lymphoma cells. To our knowledge, this represents the first case of a complication due to the progression of multicentric Castleman's disease requiring surgical intervention for intussusception.
多中心性Castleman病是一种罕见的系统性非克隆性淋巴结增生疾病。由于其与人类疱疹病毒8(HHV8)密切相关,多中心、更具侵袭性的形式可能会进展为卡波西肉瘤或非霍奇金淋巴瘤。虽然手术可治愈局限性Castleman病,但弥漫性形式的手术治疗至今仍不尽人意。我们报告了一例患者,其餐后呕吐持续1个月,符合回肠末端套叠继发部分小肠梗阻。小肠切除显示有一个狭窄性肿瘤引发了套叠。病理检查发现肿瘤由HHV8阳性的浆母细胞淋巴瘤细胞组成。据我们所知,这是首例因多中心性Castleman病进展导致套叠需手术干预的并发症病例。