Fenton James, Veenstra Michelle, Bove Paul
Department of Vascular Surgery William Beaumont Hospital, Royal Oak, MI.
Department of Vascular Surgery William Beaumont Hospital, Royal Oak, MI.
Ann Vasc Surg. 2014 Feb;28(2):490.e1-4. doi: 10.1016/j.avsg.2013.03.016. Epub 2013 Nov 5.
Primary angiosarcoma of the aorta is a rare malignancy that is characterized by rapid proliferation and propensity for metastasis. It has been reported only 35 times in the surgical literature. This case report presents a 66-year-old man diagnosed with angiosarcoma of his native aorta 7 years after endograft repair of an abdominal aortic aneurysm. We then reviewed the world surgical literature for occurrence, tumorigenic studies, prognosis, and management of aortic angiosarcoma. Because native aortic tissue is retained after endovascular repair of an abdominal aortic aneurysm, the treating physician should have an awareness of this pathology and entertain the diagnosis as appropriate.
原发性主动脉血管肉瘤是一种罕见的恶性肿瘤，其特征为快速增殖和易于转移。在外科文献中仅报道过35例。本病例报告介绍了一名66岁男性，在腹主动脉瘤腔内修复术后7年被诊断为原发性主动脉血管肉瘤。我们随后查阅了世界外科文献，以了解主动脉血管肉瘤的发病情况、肿瘤发生学研究、预后及治疗。由于腹主动脉瘤腔内修复术后仍保留了主动脉的天然组织，治疗医生应了解这种病理情况并在适当的时候考虑作出诊断。
