Purkayastha S
Department Imaging Sciences and Interventional Radiology, AMRI Hospital; Kolkata, India -
Neuroradiol J. 2008 Jun 3;21(3):306-8. doi: 10.1177/197140090802100302.
Worster-Drought syndrome (WDS) (congenital bilateral perisylvian syndrome, congenital pseudobulbar paresia) is characterized by neuronal migration defect, pseudobulbar paralysis, epilepsy, neuromotor retardation and perisylvian dysplasia. Pituitary abnormalities are rare disorders. We describe one case with an interesting association of congenital bilateral perisylvian syndrome with pituitary hypoplasia and posterior pituitary ectopia.
沃斯特-德劳特综合征(WDS)(先天性双侧外侧裂周综合征、先天性假性延髓麻痹)的特征为神经元迁移缺陷、假性延髓麻痹、癫痫、神经运动发育迟缓以及外侧裂周发育异常。垂体异常是罕见疾病。我们描述了一例先天性双侧外侧裂周综合征合并垂体发育不全及垂体后叶异位的有趣病例。