Al-Najar Mahasen, Al-Hadidy Azmy, Saleh Alaa, Al-Tamimi Ahmad, Al-Darawish Asaad, Obeidat Fatima
Department of Diagnostic Radiology, The University of Jordan Hospital, Amman, Jordan.
Sultan Qaboos Univ Med J. 2013 Nov;13(4):597-600. doi: 10.12816/0003324. Epub 2013 Nov 8.
Intraventricular hemangioblastoma (HB) is very rare; few cases of intraventricular HB have been reported in the literature, either sporadically or in association with von Hippel-Lindau disease. Furthermore, the incidence of ventricular haemorrhage from HB seems to be uncommon. We report a unique case of sporadic HB of the right lateral ventricle presenting with intratumoural and intraventricular haemorrhage in addition to multifocal intracranial superficial siderosis, indicating the presence of a subarachnoid haemorrhage (SAH) as well. Such a combination has not been reported before. In the future, the detection of an intraventricular mass in association with ventricular haemorrhage, with or without SAH, should include HB as a differential diagnosis, particularly when the imaging appearances are not typical of the more common intraventricular tumours.
脑室内血管母细胞瘤(HB)非常罕见;文献中鲜有散发性或与冯·希佩尔-林道病相关的脑室内HB病例报道。此外,HB导致脑室出血的发生率似乎并不常见。我们报告了一例独特的右侧脑室散发性HB病例,该病例除多灶性颅内表面铁沉积症外,还伴有肿瘤内和脑室内出血,这也提示存在蛛网膜下腔出血(SAH)。这种情况此前未见报道。未来,当检测到伴有或不伴有SAH的脑室出血相关的脑室内肿块时,鉴别诊断应包括HB,尤其是当影像学表现不符合更常见的脑室内肿瘤时。