Division of Cardiac Surgery, The Ohio State University Wexner Medical Center, Columbus, Ohio.
Ann Thorac Surg. 2013 Dec;96(6):2243-5. doi: 10.1016/j.athoracsur.2013.04.106.
We report a patient with congenital absence of the left pericardium with development of progressive annuloaortic ectasia and aortic insufficiency during a 12-year period. The patient was treated with a Bentall procedure. Pathologic examination of the aorta revealed cystic medial necrosis. The surgical management and a possible association between congenital absence of pericardium and Marfan syndrome are discussed.
我们报告了 1 例先天性左心包缺失患者，在 12 年期间出现进行性主动脉瓣环扩张和主动脉瓣关闭不全。患者接受了 Bentall 手术治疗。主动脉的病理检查显示囊状中层坏死。讨论了该患者的手术治疗以及先天性心包缺失与马凡综合征之间的可能关联。
