Chaurasia Jai Kumar, Soni Mayank, Ahmed Murad, Naim Mohammed
Department of Pathology, Jawaharlal Nehru Medical College (JNMC), Aligarh Muslim University (AMU), Aligarh, Uttar Pradesh, India.
BMJ Case Rep. 2013 Dec 17;2013:bcr2013201180. doi: 10.1136/bcr-2013-201180.
A 5-month-old male infant presented with a 15 day history of distension of abdomen. On clinical examination, a soft lump was palpable in the left lumbar region. Radiological findings suggested an enlarged non-functional left kidney with ureteropelvic adhesive obstruction. The left renal mass was excised and submitted for histopathological examination. The excised renal mass was cystic with its wall partly white and partly blue. Gross and histopathological findings were diagnostic of a white-blue pyelocalyceal cyst with hydrotic glomerulonephritis. This entity needs to be differentiated from a large number of other cystic diseases of the kidney. Intrauterine screening and diagnosis may be significant for a possible early intrauterine uro-laparoscopic recanalisation of the pyeloureteral obstruction to save the affected kidney.
一名5个月大的男婴，有15天的腹部膨隆病史。临床检查时，在左腰部可触及一个柔软肿块。影像学检查结果提示左肾增大且无功能，伴有肾盂输尿管粘连梗阻。切除左肾肿块并进行组织病理学检查。切除的肾肿块为囊性，其壁部分呈白色，部分呈蓝色。大体及组织病理学检查结果诊断为伴有水样变性肾小球肾炎的白-蓝肾盂肾盏囊肿。该实体需要与大量其他肾脏囊性疾病相鉴别。宫内筛查和诊断对于可能早期进行宫内输尿管肾盂镜再通术以挽救患肾可能具有重要意义。
