Perez-Negueruela Carolina, Mayol Javier, Cesar Sergi, Muchart Jordi, Segura Susana, Caffarena-Calvar Jose Maria
Department of Pediatric Cardiac Surgery, Sant Joan de Deu Hospital, Barcelona, Spain.
World J Pediatr Congenit Heart Surg. 2014 Jan 1;5(1):85-7. doi: 10.1177/2150135113512135.
The first-stage palliation of newborns with single-ventricle anatomy and transposed great arteries can be very challenging when associated with systemic ventricular outflow obstruction and aortic arch obstruction. Often, the initial intervention is a stage I Norwood procedure. We present the case of a newborn with double inlet left ventricle, discordant ventriculoarterial connection with restrictive ventricular foramen, and severe aortic arch obstruction. A hybrid procedure was performed initially as a means of addressing hemodynamic instability. Three months later, a palliative arterial switch procedure was performed as an alternative to the combined Norwood-Glenn procedure. Palliative arterial switch combined with arch reconstruction can be an effective surgical option in these complex, challenging patients.
对于具有单心室解剖结构和大动脉转位且合并体循环心室流出道梗阻和主动脉弓梗阻的新生儿,一期姑息治疗极具挑战性。通常,初始干预措施是一期诺伍德手术。我们报告一例患有双入口左心室、心室动脉连接不一致且心室孔受限以及严重主动脉弓梗阻的新生儿病例。最初进行了杂交手术以解决血流动力学不稳定问题。三个月后,进行了姑息性动脉调转手术,作为诺伍德 - 格林手术联合术式的替代方案。姑息性动脉调转联合主动脉弓重建对于这些复杂且具有挑战性的患者而言可能是一种有效的手术选择。