Kahraman Sinan, Enercan Meriç, Demirhan Ozkan, Sengül Türker, Dalar Levent, Hamzaoğlu Azmi
Istanbul Spine Center, Istanbul Florence Nightingale Hospital, 34387 Istanbul, Turkey.
Department of Thoracic Surgery, School of Medicine, Istanbul Bilim University, 34387 Istanbul, Turkey.
Case Rep Orthop. 2013;2013:987578. doi: 10.1155/2013/987578. Epub 2013 Dec 18.
Achondroplasia was first described in 1878 and is the most common form of human skeletal dysplasia. Spinal manifestations include thoracolumbar kyphosis, foramen magnum, and spinal stenosis. Progressive kyphosis can result in spinal cord compression and paraplegia due to the reduced size of spinal canal. The deficits are typically progressive, presenting as an insidious onset of paresthesia, followed by the inability to walk and then by urinary incontinence. Paraplegia can be the result of direct pressure on the cord by bone or the injury to the anterior spinal vessels by a protruding bone. Surgical treatment consists of posterior instrumentation, fusion with total wide laminectomy at stenosis levels, and anterior interbody support. Pedicle screws are preferred for spinal instrumentation because wires and hooks may induce spinal cord injury due to the narrow spinal canal. Pedicle lengths are significantly shorter, and 20-25 mm long screws are appropriate for lower thoracic and lumbar pedicles in adult achondroplastic There is no information about the appropriate length of screws for the upper thoracic pedicles. Tracheal injury due to inappropriate pedicle screw length is a rare complication. We report an extremely rare case of tracheal tear due to posterior instrumentation and its management in the early postoperative period.
软骨发育不全于1878年首次被描述,是人类骨骼发育异常最常见的形式。脊柱表现包括胸腰椎后凸、枕大孔及椎管狭窄。由于椎管尺寸减小,进行性后凸可导致脊髓受压和截瘫。这些缺陷通常呈进行性,表现为隐匿性感觉异常发作,随后出现行走能力丧失,继而出现尿失禁。截瘫可能是由于骨骼对脊髓的直接压迫或突出的骨骼对脊髓前血管的损伤所致。手术治疗包括后路内固定、在狭窄节段进行全椎板切除术并融合以及前路椎间支撑。椎弓根螺钉是脊柱内固定的首选,因为钢丝和钩子可能因椎管狭窄而导致脊髓损伤。椎弓根长度明显较短,对于成年软骨发育不全患者,20 - 25毫米长的螺钉适用于下胸椎和腰椎椎弓根。目前尚无关于上胸椎椎弓根螺钉合适长度的信息。因椎弓根螺钉长度不当导致的气管损伤是一种罕见的并发症。我们报告了1例因后路内固定导致气管撕裂的极其罕见的病例及其术后早期处理。