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1型神经纤维瘤病患者发生肩胛下动脉动脉瘤破裂及锁骨下动脉闭塞:一例报告

Ruptured subscapular artery aneurysm and subclavian artery occlusion in a patient with type 1 neurofibromatosis: a case report.

作者信息

Moreau Antoine, Joskin Julien, Kreutz Julie, Nchimi Alain

机构信息

Department of Medical Imaging, University Hospital -Sart Tilman, Domaine du Sart Tilman B35, 4000 Liège, Belgium.

出版信息

J Med Case Rep. 2014 Feb 5;8:39. doi: 10.1186/1752-1947-8-39.

Abstract

INTRODUCTION

Collateral muscular artery aneurysm is exceedingly rare. We report the first case of subscapular artery aneurysm in a patient with type 1 neurofibromatosis and ipsilateral chronic subclavian artery occlusion.

CASE PRESENTATION

A 74-year-old Caucasian woman with a medical history of type 1 neurofibromatosis, presented a sudden left pectoral mass, later diagnosed as a ruptured aneurysm of the left subscapular artery. It was caused by a chronic occlusion of the left subclavian artery, diagnosed on angiographies prior to embolization.

CONCLUSIONS

Collateral artery aneurysm in the event of a mainstream muscular artery chronic occlusion may occur in type 1 neurofibromatosis.

摘要

引言

侧支肌性动脉瘤极为罕见。我们报告首例1型神经纤维瘤病患者并发同侧慢性锁骨下动脉闭塞时出现肩胛下动脉瘤的病例。

病例介绍

一名74岁患有1型神经纤维瘤病的白种女性,突发左胸肿块,后诊断为左肩胛下动脉破裂性动脉瘤。其病因是左锁骨下动脉慢性闭塞,在栓塞术前血管造影检查中得以确诊。

结论

1型神经纤维瘤病患者在主干肌性动脉发生慢性闭塞时可能出现侧支动脉瘤。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/0404/3923555/43d7747b47ee/1752-1947-8-39-1.jpg

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