The proximal tubule in cystinosis: fight or flight?
作者信息
Chevalier Robert L
机构信息
Department of Pediatrics, the University of Virginia, Charlottesville, Virginia
出版信息
J Am Soc Nephrol. 2014 Jun;25(6):1131-2. doi: 10.1681/ASN.2014010058. Epub 2014 Feb 13.
Abstract
摘要
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本文引用的文献
1
Time course of pathogenic and adaptation mechanisms in cystinotic mouse kidneys.
J Am Soc Nephrol. 2014 Jun;25(6):1256-69. doi: 10.1681/ASN.2013060598. Epub 2014 Feb 13.
2
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J Am Soc Nephrol. 2014 Jun;25(6):1163-9. doi: 10.1681/ASN.2013060653. Epub 2014 Feb 13.
3
Responses of proximal tubular cells to injury in congenital renal disease: fight or flight.
Pediatr Nephrol. 2014 Apr;29(4):537-41. doi: 10.1007/s00467-013-2590-9. Epub 2013 Aug 16.
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Renal functional decline and glomerulotubular injury are arrested but not restored by release of unilateral ureteral obstruction (UUO).
Am J Physiol Renal Physiol. 2013 Feb 15;304(4):F432-9. doi: 10.1152/ajprenal.00425.2012. Epub 2012 Dec 5.
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Fight-or-flight: murine unilateral ureteral obstruction causes extensive proximal tubular degeneration, collecting duct dilatation, and minimal fibrosis.
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Am J Physiol Renal Physiol. 2011 Jul;301(1):F110-7. doi: 10.1152/ajprenal.00022.2011. Epub 2011 Mar 23.
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The pathogenesis of cystinosis: mechanisms beyond cystine accumulation.
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