The University of Texas Health Science Center at San Antonio, San Antonio, Texas.
Dermatol Ther. 2013 Nov-Dec;26(6):439-44. doi: 10.1111/dth.12106.
Aplasia cutis congenita (ACC) refers to any condition in which there is absence of skin at birth. This can be isolated ACC occurring on the scalp, with or without underlying ectopic neural tissue, or ACC can be associated with other conditions such as Adams-Oliver syndrome or epidermolysis bullosa. We discuss the different types of ACC and associated anomalies along with an approach to diagnosis and management.
先天性皮肤发育不全(ACC)是指出生时即存在皮肤缺失的任何情况。这种情况可以是孤立性 ACC,发生在头皮上,伴有或不伴有异位神经组织,也可以与其他情况相关,如亚当-奥利弗综合征或大疱性表皮松解症。我们讨论了不同类型的 ACC 及其相关畸形,并介绍了诊断和治疗方法。