AbdollahiFakhim Shahin, Bayazian Gholamreza, Notash Rezvan
Department of Pediatrics Otolaryngology, Pediatrics Hospital, Tabriz University of Medical Sciences, Tabriz, Iran.
Department of Pediatrics Otolaryngology, Pediatrics Hospital, Tabriz University of Medical Sciences, Tabriz, Iran.
Int J Pediatr Otorhinolaryngol. 2014 Apr;78(4):697-700. doi: 10.1016/j.ijporl.2014.01.027. Epub 2014 Jan 31.
Lipoma is the most common soft tissue mass in adults but it is uncommon in children. Nasal septal lipoma is an even more rare entity. In this report, a 12-year-old girl was presented with congenital nasal septal lipoma. She had permanent partial nasal obstruction on her right side and disfigurement of her right upper lip. CT scan revealed a lipoma-like mass in the septum plus an additional incidental finding of an intracranial lipoma. Further workup with MRI demonstrated corpus callosum agenesis with interhemispheric lipoma. To remove the mass, septoplasty, nasal lipoma excision and nasal vestibule V-Y advancement flap were performed. To close the lip a rotational advancement flap was required. Our case seemed to be a variety of Pai syndrome. We recommend imaging of the central nervous system in newborns with congenital lipomas located in the craniofacial midline to rule out the Pai syndrome.
脂肪瘤是成人中最常见的软组织肿块，但在儿童中并不常见。鼻中隔脂肪瘤更是罕见。在本报告中，一名12岁女孩被诊断为先天性鼻中隔脂肪瘤。她右侧有永久性部分鼻塞，右上唇有畸形。CT扫描显示鼻中隔有一个脂肪瘤样肿块，另外还意外发现了一个颅内脂肪瘤。进一步的MRI检查显示胼胝体发育不全伴半球间脂肪瘤。为切除肿块，进行了鼻中隔成形术、鼻脂肪瘤切除术和鼻前庭V-Y推进皮瓣手术。为闭合唇部，需要一个旋转推进皮瓣。我们的病例似乎是派综合征的一种。我们建议对颅面中线有先天性脂肪瘤的新生儿进行中枢神经系统成像，以排除派综合征。
