Li Jui-Ting, Dai Yang-Hong, Kuo Shih-Ming
Department of Paediatric Surgery, Tri-Service General Hospital, Taipei, Taiwan.
BMJ Case Rep. 2014 Mar 26;2014:bcr2014203904. doi: 10.1136/bcr-2014-203904.
Neuroblastoma is the second most common retroperitoneal tumour in children after Wilms' tumour. When it originates in the retroperitoneum, neuroblastoma usually presents as an abdominal mass with clinical manifestations of nausea, vomiting and weight loss. Imaging studies of this tumour demonstrate a heterogeneous mass with an irregular capsule and visible calcifications. Encasement and compression of the abdominal vessels, especially the inferior vena cava, are often observed. However, stenosis of the inferior vena cava has never been reported to be associated with this tumour. Here, we present a case of a 5-month-old boy with a right retroperitoneal tumour with extensive encasement of the inferior vena cava and significant narrowing of its distal part between the venous bifurcation and the tumour capsule. To our knowledge, this is the first case of neuroblastoma with this manifestation in a child.
神经母细胞瘤是儿童中仅次于肾母细胞瘤的第二常见的腹膜后肿瘤。当神经母细胞瘤起源于腹膜后时，通常表现为腹部肿块，并伴有恶心、呕吐和体重减轻等临床表现。该肿瘤的影像学检查显示为一个具有不规则包膜和可见钙化的不均匀肿块。常观察到腹部血管，尤其是下腔静脉被包裹和受压。然而，从未有报道称下腔静脉狭窄与该肿瘤有关。在此，我们报告一例5个月大的男孩，患有右腹膜后肿瘤，下腔静脉被广泛包裹，且在静脉分叉与肿瘤包膜之间的远端部分明显变窄。据我们所知，这是首例儿童神经母细胞瘤出现这种表现的病例。
