Plexiform neurofibroma of uterus: a rare manifestation of neurofibromatosis 1.

Neurofibromatosis type 1 (NF1) rarely affects the female genital system. Plexiform neurofibromas are congenital lesions that occur exclusively in patients with neurofibromatosis type I. The vulva is the most frequent genital organ to be affected, whereas vaginal, cervical, uterine, and ovarian neurofibromas have also been reported only rarely. We present an 8 years old girl with plexiform neurofibroma primarily involving genital system.