1 The Russell H. Morgan Department of Radiology and Radiological Science, Johns Hopkins Hospital, 601 N Caroline St, Baltimore, MD 21287.
AJR Am J Roentgenol. 2014 May;202(5):1120-9. doi: 10.2214/AJR.13.11485.
Arterial dissection and aneurysm rupture are significant sources of morbidity and mortality in patients with connective tissue diseases. This article provides a detailed analysis of cardiovascular involvement in Marfan syndrome, Loeys-Dietz syndrome, and vascular Ehlers-Danlos syndrome.
Although these syndromes share some overlapping features, they have discriminating clinical and imaging features, and knowledge of these features enables the radiologist to aid the referring clinician in making the correct diagnosis.
在结缔组织疾病患者中，动脉夹层和动脉瘤破裂是发病率和死亡率的重要来源。本文详细分析了马凡综合征、Loeys-Dietz 综合征和血管型 Ehlers-Danlos 综合征的心血管受累情况。
尽管这些综合征具有一些重叠特征，但它们具有明显不同的临床和影像学特征，了解这些特征可使放射科医生帮助临床医生做出正确诊断。
